【摘要】 嗜铬细胞瘤和副神经节瘤(paragangliomas,PPGLs)是罕见的神经内分泌肿瘤，分别起源于肾上腺髓质或肾上腺外副神经节，可产生儿茶酚胺。2017版WHO《内分泌器官肿瘤分类》和2022版WHO《内分泌和神经内分泌肿瘤分类》认为所有副神经节瘤均被视为恶性肿瘤，具有类似于上皮性神经内分泌肿瘤的可变转移潜能。通过对副神经节瘤伴儿茶酚胺心肌病案例的分析，应编码为：E88.907I43.1*代谢性心肌病；E27.500x003儿茶酚胺分泌过多；C48.000x001腹膜后恶性肿瘤；M86800/3恶性节旁体瘤。遇到疑难编码时，病案科应组织专题研讨会，加强与临床、病理等科室的沟通，完善质控流程，建立编码考核制度，持续提升编码质量。更多还原

【Abstract】 Pheochromocytomas and paragangliomas(PPGLs) are rare neuroendocrine tumors arising from the adrenal medulla or extra-adrenal paraganglia, respectively, which produce catecholamines. According to the 2017edition of WHO “Classification of Endocrine Organ Tumors” and the 2022 edition of WHO “Classification of Endocrine and Neuroendocrine Tumors”, all paragangliomas are regarded as malignant tumors with variable metastatic potential similar to epithelial neuroendocrine tumors. Through the analysis of paraganglioma with catecholamine cardiomyopathy, the correct disease code:E88.907 I43.1*;E27.500X003;C48.000x001;M86800/3.When encountering coding difficulties, the medical records department should strengthen communication with clinical, pathological and other departments, improve quality control processes, establish a coding evaluation system, and continuously improve coding quality. When accounting for differential coding, the medical records department should organize special seminars, strengthen communication with clinical, pathological and other departments, improve quality control processes, establish coding assessment systems, and continuously improve coding quality.更多还原