【摘要】 目的分析烟雾病的临床表现及影像学表现,探讨双源Flash CT血管造影及其后处理技术在烟雾病诊断中的应用价值。方法对本院2013年1月~2014年7月收治的21例烟雾病患者的临床特点及影像检查资料进行回顾性分析。结果 1烟雾病发病年龄在17~42岁左右,40岁以前占90%,临床表现以缺血为主,肢体无力和偏瘫最为常见。2CT提示:脑梗死13例,脑出血6例,脑出血合并脑梗死2例。CT血管造影及DSA示双侧或单侧颈内动脉、大脑前动脉及大脑中动脉管腔狭窄或闭塞,脑基底部异常血管网形成,如烟雾状。结论对于儿童及青年人反复出现脑缺血发作、脑出血、脑梗死,应高度怀疑烟雾病,CT血管造影可作为首选检查方法,临床怀疑病例及早行DSA检查。更多还原

【Abstract】 Objective To analyze the clinical manifestation and imaging manifestation of moyamoya disease, and to explore the application value of double source Flash CT angiography and its post-processing technique in the diagnosis of moyamoya disease. Methods Clinical characteristics and data of imaging examination of 21 patients with moyamoya disease who were admitted to our hospital from January 2013 to July 2014 were retrospectively analyzed. Results1 Age of onset of moyamoya disease was around 17-42 years old, and patients younger than 40 years old accounted for90% of the total. The clinical manifestation was mainly ischemia, and weakness of limbs and hemiplegia were the most commonly seen. 2CT indicated that 13 patients were cerebral infarction, 6 patients were cerebral bleeding, and 2 patients were cerebral bleeding complicated with cerebral infarction. CT angiography and DSA showed stenosis or blocking of bilateral or unilateral internal carotid artery, anterior cerebral artery and middle cerebral artery, and showed the formation of abnormal vessel network at the base of the brain like smoke. Conclusion For children and adults who have repeated occurrence of transient ischemic attack, cerebral bleeding, and cerebral infarction, moyamoya disease should be highly suspected. CT angiography can be selected as the first choice of examination, and DSA examination should be performed timely for clinically suspected cases.更多还原