【摘要】 目的探讨双侧输尿管末段狭窄性梗阻致尿闭的临床特点、诊断及治疗。方法先天性双侧输尿管末段狭窄患儿7例,男2例,女5例,年龄35~57 d。临床表现为突发性尿闭或少尿,均行B超、膀胱造影及肾盂穿刺造影,3例行磁共振尿路水显像,诊断明确后行输尿管狭窄段切除、输尿管再植术。结果7例患儿均经肾盂穿刺造影确诊,一期手术后6例治愈,随诊2~4年未发现输尿管狭窄及返流发生,肾功能恢复良好;1例症状复发,二次手术后治愈。结论对生后突发尿闭患儿应考虑先天性双侧输尿管末段狭窄的可能,肾盂穿刺造影及磁共振尿路水显像可明确诊断,输尿管狭窄段切除、输尿管再植术是有效的治疗方法。更多还原

【Abstract】 Objective To investigate the clinical features of anuria caused by pediatric congenital bilateral ureteral stenotic obstruction,and to improve the diagnosis and treatment of the disease.Methods This series included 7 infants(2 males and 5 females;age range,35-57 d) with congenital bilateral ureteral stenotic obstruction.The clinical presentations were characterized by sudden anuria or oliguria.B-ultrasound,cystography and puncture pyelography were performed in all of them,and magnetic resonance urography(MRU) in 3.Based on the definite diagnosis,resection of stenotic segment of the ureter or ureteral implantation was performed on them.Results The diagnosis was confirmed by puncture pyelography in all of the 7 cases.Six cases underwent phase I surgery and recovered.No ureteral stenosis and cystoureteral reflux occurred during a follow-up of 2-4 years.The renal function was normalized in them.One case had stenosis recurrence due to scar formation,and was cured by the second operation.Conclusions Anuria caused by pediatric congenital bilateral ureteral stenosis should be diagnosed and treated as early as possible.Definite diagnosis can be established by puncture pyelography and MRU.Resection of the obstructive segment of the ureter,protection of renal function,and ureteral implantation are the main therapies.更多还原