【摘要】 目的　报道 4例口周色素沉着 肠息肉综合征病例的临床表现、病理特征 ,及对其家族史进行追踪观察。方法　通过临床观察、X线检查、病理诊断、家族史作出分析。结果　口周色素沉着 肠息肉综合征具有家族遗传现象。肠道病变部位与恶变有相关性。结论　发现病症需作家族遗传学调查。病变发生在结肠者为高危区 ,需作长期定时监护。更多还原

【Abstract】 Objective Four patients with Peutz-Jeghers syndrone were consecutively observed according to their clinical manifestation, pathologic characteristic, family history.Methods Four cases were analyzed according to their clinical observation, X-ray detection, pathological diagnosis and family history. Results Peutz-Jeghers syndrone had characteristic of family inheredity. Intestinal leison was correlative to canceration of polypus.Conclusion Family inhereditary detection should be performed in Peutz-Jeghers syndrone patients. The patients whose intestinal leison was located in colon were considered high risk patients. They should be intensively cared regularly in long-term.更多还原