【摘要】 目的总结婴儿型肝脏血管内皮细胞瘤的CT表现和随访变化,为指导临床制定治疗方案提供依据。方法回顾性分析7例婴儿型肝脏血管内皮细胞瘤,包括首次就诊和随访的CT表现。患儿年龄11天～60天,男性2例,女性5例。所有病例均行CT平扫和增强扫描。结果CT平扫肿瘤表现为肝内多发或单发的边界清晰的低密度病灶,增强扫描早期可见肿瘤呈显著结节状强化、不均匀强化或边缘强化,延迟期扫描可见肿瘤由周边向中心递进强化的特征。巨大病灶的中央坏死区可始终无强化,并可见斑片钙化灶。给予类固醇皮质激素治疗后,CT随访(6例)病灶均不同程度缩小,部分病灶完全消失。结论婴儿型肝脏血管内皮细胞瘤表现为多发病灶和单发病灶,CT显示为多发强化结节或边缘强化的巨大病灶,激素治疗肿瘤可自行退化或消失。更多还原

【Abstract】 Objective To summarize the initial CT findings and follow-up of infantile hepatic hemangioendothelioma(IHHE), for helping to make clinical treatment strategies. Methods We retrospectively analyzed the clinical,the initial and follow-up CT imaging features in 7 cases of IHHE, all of which have underwent noncontrast and postcontrast CT scans. Results At noncontrast CT, the IHHE manifested as single or multiple, well-defined and hypodense masses. At postcontrast CT, the enhancement patterns of IHHE included nodular,heterogeneous or peripheral enhancement in the early phase, subsequent central enhancement with variable delay scans. In larger tumors, central necrosis with calcifications lacks enhancement in all of phrases. The follow-up CT scans of 6 cases given steroids showed the masses shrinked strikingly or disappeared completely. Conclusion The typical imaging features of IHHE include two types: singe, giant mass with peripheral enhancement or multiple lesions with nodular enhancement. Given steroids, the IHHE has a natural history of regression and involution. Especially the multiple lesions tend to disappear completely within one year.更多还原