【摘要】 目的探讨幕上原始神经外胚层肿瘤(PNET)的MRI表现,以期提高对本病的诊断水平。方法回顾分析14例经手术和病理证实的幕上PNET的MRI表现,并与手术病理相对照。结果病灶位于顶叶4例,额叶3例,枕顶叶2例,颞枕叶3例,侧脑室1例,鞍区1例,病灶普遍较大,病灶绝大多数信号不均匀,病灶内可见囊变坏死(12例)、出血(2例)、流空小血管影(6例),增强后病灶呈明显不均匀强化(12例),中等强化2例;神经母细胞瘤10例,节细胞神经母细胞瘤3例,非典型横纹肌样瘤1例。结论颅内PNET的MRI表现有一定特点,MRI有助于该病的诊断和指导治疗;最后的确诊依赖于病理学诊断。更多还原

【Abstract】 Objective To analyze the magnetic resonance imaging (MRI) features of supratentorial primitive neuroectodermal tumors (sPNET) and improve the diagnosis of this disease. Methods MRI manifestations of 14 cases of PNET were retrospectively analyzed and compared with their pathological features. Results The supratentorial lesions involved the occipital lobe in 4, frontal lobe in 3, fronto-occipital lobe in 2, temporo-occipital lobe in 3, lateral ventricle in 1 case and the saddle region in 1. All the lesions were large in volume and most of them presented heterogeneous signals in MRI. Of the 14 cases, 12 showed cystic degeneration and necrosis, 2 had hemorrhage and 6 showed signs of emptied small blood vessels. Twelve cases had heterogeneous enhancement and 2 had moderate enhancement. Pathologically, 10 cases of neuroblastomas were identified, along with 3 ganglioneuroblastomas and 1 atypical rhabdoid tumor. Conclusion MRI findings of PNET are rather characteristic to assist in the diagnosis and treatment of the disease, but a final definite diagnosis still relies on pathological examination.更多还原