【摘要】 目的探讨消失肺综合征的CT诊断价值。方法对13例消失肺综合征患者的临床表现、CT图像(包括手术前后HRCT)综合分析。并对全部患者家庭成员进行胸透或胸片或HRCT普查。结果13例患者(男9例,女4例)中3例为家族性发病,10例为散发性。4例有或曾有自发性气胸史。4例行胸腔闭式引流术,6例行肺大泡摘除术,1例行肺减容术。该组病例按3型分法属单发型2例,多发型6例,弥漫或毁损型5例。结论C(T包括HRCT)扫描对该病的诊断、治疗方案的选择及预后评价均有重要的指导作用。更多还原

【Abstract】 Objective To explore the value of CT in the diagnosis of vanishing lung syndrome. Methods CT imagine, clinical presentations, pre-and postoperative HRCT image of 13 cases were analyzed. All family members of familial vanishing lung syndrome were screened with fluoscopy, radiography or HRCT. Results Three of thirteen patients (male 9, female 4) were familial. 4 cases had pneumothrax or had a history of it, 4 cases underwent thoracic cavity closed drainage therapy, 6 cases underwent pulmonary bullae extirpation, 1 case underwent lung volume reduction surgery. Patients were divided into three types according to the imaging findings and clinical appearance 1 : single type (n =2); multiple type (n =6); diffused or destructive lung type. Conclusion CT (HRCT) is valuable in clinical diagnosis, treatment planning and prediction of the prognosis.更多还原