【摘要】 目的分析外周原始神经外胚层肿瘤(pPNET)的CT和MR I表现,以期提高对该病的认识。方法回顾性分析6例经病理诊断的外周原始神经外胚层肿瘤的CT和MR I表现。男4例,女2例,其中起源于骨组织2例,软组织pPNET 4例。结果骨组织pPNET表现为溶骨性骨质破坏伴有软组织肿块,病灶CT呈等密度,MR I T1W I等信号,T2W I等、高信号,增强明显但不规则,无明显瘤骨和骨膜反应;软组织pPNET病灶体积比较大,直径>6 cm,CT等密度,MR I T1W I等、低信号,T2W I等、高信号,增强明显,对周围正常组织有侵袭,无钙化。2例有明显的坏死。结论pPNET的CT和MR I表现缺乏特征性,但有助于本病良恶性鉴别、判断手术可切除性、检出远处转移和评价治疗效果。更多还原

【Abstract】 Objective To describe the imaging features of peripheral primitive neuroectodermal tumor（pPNET）.Methods CT andMRI imagings in six patients with pPNET proved pathologically were reviewed retrospectively.Four were male,others were female.Twocases lvcalized in came from the bone,the rest in soft tissue.Results pPNET in bone showed lytic lesion with soft tissue mass.The lesion presented isodensity on CT and isointensity on T₁WI and isoor hyperintensity on T₂WI.In 1 case with contrast enhancement,marked heterogeneous enhancement was present.There was periosteal reaction.pPNET in soft tissue appeared as a large masses which were larger than 6 cm in diameter.The lesion showed iso density on CT imagings and iso-or hypointensity on T₁WI,iso-or hyperintensity on T₂WI and marked enhancement.Surrounding normal tissues were invaded without calcification.2 of all had necrosis markedly.Conclusion Although CT and MRI findings of pPNET are nonspecific,the imaging is useful in differentiating the nature of tumor,predicting resectiblity,detecting distant metastases and evaluating treatment.更多还原