【摘要】 POEMS综合征和遗传性神经纤维瘤病I型(NFⅠ)是不同病因不同发病机制致病的两种疾病,但均可引起多系统损害,症状体征有交叉,二者合并病例很罕见。本文报告了近期收治的以多发周围神经病和多发皮肤损害为首发症状的遗传性神经纤维瘤病I型伴POEMS综合征的病例,并讨论了POEMS综合征和NFⅠ的多发周围神经病和多发脏器损害的特点。更多还原

【Abstract】 POEMS syndrome and hereditary neurofibromatosis type I (NF I) are two different diseases with different causes and pathogenesis but both can cause multiple system lesions. The coexisting case was rare. Here we reported a case of hereditary NF I with POEMS syndrome. Polyneuropathy and skin lesions were first presented in this patient. The features of polyneuropathy and multiple organ lesions of POEMS syndrome and hereditary NF I were reviewed based on the case in this paper.更多还原