【摘要】 目的　探讨肾源性尿崩症所致巨输尿管 巨膀胱综合征的临床特点及诊治措施。　方法　分析 1999年 12月收治的 1例病历资料 ,结合文献复习讨论。　结果　病人为重度尿路积水 ,血生化、血电解质正常 ,尿比重 1.0 0 0。尿动力学检查和肾动态显影未见尿路梗阻表现。利钠利尿剂等药物有助于减少患者尿量。治疗后随访 6个月 ,患者尿量 5 0 0 0～ 6 0 0 0ml。B超复查肾盂积水较治疗前有所减轻 ,膀胱剩余尿量明显减少。　结论　肾源性尿崩症导致巨输尿管 巨膀胱综合征合并尿路破裂者罕见 ,药物治疗可明显减少尿量 ,减轻和阻止尿路积水的发生。临床早期诊断采取防治措施十分重要。更多还原

【Abstract】 Objective To study the clinical features and the urological complications of congenital diabetes insipidus. Methods A case of congenital diabetse insipidus was presented with review of the li- terature.The urodynamics and the isotopic renal dynamic imaging of the patient were studied. Results The patient had megahydronephrosis,megaureter and megacystis with very low specific gravity of the urine (1.000) yet with normal blood chemistry,normal blood electrolytes and with no urinary tract outflow obstruction.The urine volume could be decreased by medication. Conclusions Early diagnosis of congenital diabetes insipidus and the prevention of urological complications are important.Automatic urinary tract rupture secondary to congenital diabetes insipidus is rarely seen.更多还原