【摘要】 目的　研究肺动脉闭锁合并室间隔缺损的体肺侧支血管和肺动脉的发育情况及其临床意义。方法　回顾研究 98例肺动脉闭锁合并室间隔缺损的右心室和主动脉 (弓降部及降部上段包括6 3例选择性侧支血管 )造影所见 ,着重分析体肺动脉侧支血管的类型和左、右肺动脉的发育情况 ,有无融合等。结果　 98例中由未闭的动脉导管供血者 14例 (14% ) ,其中婴幼儿 11例。直接主 肺动脉侧支供血 43例 (4 4% ) ,多种侧支供血 41例 (4 2 % )。 98例中 6 0例通过侧支血管供血 ,可见左、右肺动脉显影且均有融合 ,其中 2 6例左或 (和 )右肺动脉发育不良。结论　右心室和主动脉造影结合必要的选择性侧支血管造影仍是显示体肺侧支供血和肺动脉发育的重要方法更多还原

【Abstract】 Objective To evaluate the angiography in demonstrating the development of systemic pulmonary collateral vessels and pulmonary arteries, and its clinical significance in pulmonary atresia with ventricular septal defect (PA+VSD). Methods The findings of angiography of the right ventricle and aorta arch and upper portion of the descending thoracic aorta in 98 cases with PA+VSD were retrospectively studied including 63 additional selective angiography of collateral vessels. The types of systemic pulmonary collateral vessels and the development of left and right native pulmonary arteries with or without fusion were emphatically analyzed, etc. Results Among those 98 cases, the pulmonary arteries were supplied by patent ductus arteriosus in 14(14%), 11 of them were infants and young children; and by direct aortopulmonary collaterals in 43(44%); by multiple origin of systemic pulmonary artery collaterals in 41(42%). 60 of 98 cases were visualized the presence of left and right native pulmonary arteries through collateral vessels. Among them, the hypoplasia of left and/or right pulmonary arteries was found. Conclusion Angiography of right ventricle and aorta combined with necessary selective angiography of collateral vessels was still an indispensable method in the demonstration of systemic pulmonary collateral vessels and development of pulmonary arteries, and provided the main basis for the selection of indications for interventional/surgical therapy.更多还原