【摘要】 患者女 ,2 2岁。自幼于左面部出现褐色角化性油腻斑 ,逐渐扩大波及上半身。家族中父亲及一挛生妹妹身上有较轻的类似皮损。查体右眼轻度斜视。皮疹呈环形堤状隆起 ,褐色角化斑 ,部分皮疹匐行性延长呈条索状或地图状 ,与肢体长轴呈平行排列 ,背部左侧呈单侧分布 ,其余部位对称分布。组织病理检查示汗孔角化症。更多还原

【Abstract】 A 22 year old female presented oily brown keratinized macula at left face at birth which increased in size with age In her family her father and her twin sister had the similar mild lesions The right eye had slightly oblique vision The lesions were keratinized, ring , dammed and swelled up, part of those crawled to striplike and maplike and paralleled with the long axes of the limbs The lesions of left back were distributed only on one side, the other lesions were symmetrical The characteristics of the histopathologic feature of the lesions confirmed the diagnosis更多还原