【作者】 王衡健； 袁捷； 张英； 韦敏； 祁佐良；

【Author】 HengJian Wang,Jie Yuan,Ying Zhang,Min Wei,ZuoLiang Qi

【机构】 上海第九人民医院；

【摘要】 面中份发育不全即Binder综合征是一组以面中份发育不全和鼻畸形为主要表现的先天性畸形。临床表现主要包括面中份凹陷,"圆盘脸"和鼻畸形,鼻畸形主要有鼻扁平、鼻小柱过短等。治疗主要是通过手术纠正面中份后缩和鼻畸形。手术方法根据畸形严重程度不同而改变,包括单纯鼻充填、面中份截骨前移和两者结合。本文报道了本科室8例Binder患者手术治疗的经验,术式采用改良的鼻-上颌-硬腭"厢形"截骨联合鼻充填术。术后患者对手术效果满意,没有严重并发症发生,术后6个月回访发现面中分前移骨块固位良好,假体固位牢靠,无明显吸收、变形,面中分外形良好,鼻外形、突度保持良好,鼻唇角正常。结果提示鼻-上颌-硬腭截骨辅助鼻充填技术是纠正面中分畸形较好的选择,在治疗Binder综合征中可以获得满意地临床疗效。更多还原

【Abstract】 Maxillofacial dysplasia,or Binder’s Syndrome is a congenital condition consisting of midifacial hypoplasia with a characteristic of flat nasal deformity.Surgical approach is mainly varied with degree of deformity, overall goals is to advance skeletal dysplasia of the midface and correct flat nose with various graft implant.In our study, we reported 8 patients with maxillonasal dysplasia of variable degrees using modified nasomaxillary complex and hard palatine "box" osteotomy,combined with chondrocostal bone grafts or nasal implant to correct the retruded nasal deformity.The technique has been used in all patients with ages and degree of deformity.All patients were satisfied with outcome of operation,no severe complication was found.6-months follow-up evaluation showed good correction of the midface profile and nasal projection,the advancement of midface was found stable,chondrocostal bone graft was fixed perfectly,no obvious absorption and remodeling was found in short time.As result showed modified nasomaxillary complex and hard palatine "box" osteotomy can be a good alternative for advancement of midfacial hypoplasia,nasal implant is a perfect option to correct nasal deformity of Binder’s syndrome and both can satisfy requirement of patients.更多还原