【作者】 李倩；

【导师】 杨蓓蓓；

【作者基本信息】 浙江大学 ， 耳鼻咽喉科学（专业学位）， 2013， 硕士

【摘要】 前庭导水管扩大(Enlarged Vestibular Aqueduct, EVA)是临床上最常见引起儿童感音神经性聋的先天性内耳畸形,临床表现为患耳波动性听力下降伴或不伴前庭症状,其发病机制仍处于研究阶段,颞骨高分辨CT及头颅MRI可辅助诊断。该疾病致患耳最终发展成极重度聋,保守治疗无法使患者从中获益。近30年来,人工耳蜗植入(Cochlear Implant, CI)手术逐渐成为治疗前庭导水管扩大综合征的唯一有效方法。为正确了解前庭导水管扩大综合征,做到早期发现、早期干预、有效治疗,本文报道5例前庭导水管扩大综合征病例,并复习前庭导水管扩大综合征的相关文献,主要从发病机制及治疗进展进行文献综述。更多还原

【Abstract】 Enlarged vestibular aqueduct is one of the most common clinical congenital deformities of the inner ear, The clinical manifestation is fluctuating hearing loss associated with vestibular symptoms or not, and its pathogenesis is still in research stage, and the temporal bone high resolution computed tomography (HRCT) and cranial magnetic resonance imaging (MRI) have importance accessory diagnostic value. The hearing of the ear will develop into profound deafness eventually, and patients can hardly benefit from conservative treatment. Over the past30years, cochlear implantation gradually became the only effective way to treat EVAS. In order to understand EVAS correctly, and get early discovery, intervention and effective treatment, we report5cases about EVAS, and review the related literature, mainly about the pathogenesis and treatment progress.更多还原