【摘要】 布加综合征是由各种原因引起的肝静脉流出道梗阻，导致以肝充血和门静脉高压为特征的综合征。典型肝脏病理特征为肝窦明显扩张，慢性发展可出现肝硬化。临床诊断通常依赖影像学检查提示，并通过金标准下腔静脉造影确诊。但因该病临床表现复杂多变，容易误诊漏诊，延误治疗。现报道1例先因误诊漏诊而治疗无效的布加综合征引起的肝硬化病例，最终基于肝活检病理检查发现、门静脉CT检查和下腔静脉造影得以临床确诊与有效治疗的过程，以期提高对该病的认识。更多还原

【Abstract】 Budd-Chiari syndrome is a syndrome characterized by hepatic congestion and portal hypertension due to obstruction of the hepatic venous outflow tract caused by various causes. The typical pathological feature of the liver is marked dilation of the hepatic sinus, and chronic development can lead to cirrhosis. Clinical diagnosis usually relies on imaging evidence, which then is confirmed by gold-standard inferior vena cava angiography. However, due to the complex and variable clinical manifestations of this disease, it is easy to misdiagnose or miss the diagnosis, resulting in delayed treatment. Here we report one case of cirrhosis caused by Budd-Chiari syndrome who was initially ineffectively treated due to misdiagnosis and missed diagnosis and was finally clinically diagnosed and effectively treated based on the pathological findings of liver biopsy, portal vein CT examination and inferior vena cava angiography, in order to improve the understanding of the disease.更多还原