【摘要】 甲状腺素转运蛋白淀粉样变性心肌病(ATTR-CM)是由于甲状腺素转运蛋白解离成单体后错误折叠为淀粉样物质,沉积于心肌间质而导致的一种心肌病。ATTR-CM主要分为突变型和野生型,临床表现无典型症状和体征。为提高国内在ATTR-CM的诊疗实践和临床研究,现简要介绍国内外关于ATTR-CM的最新诊断标准及治疗方法。更多还原

【Abstract】 Transthyretin amyloid cardiomyopathy is caused by the wrong folding of transthyretin into amyloid substance after dissociation into monomer and deposition in myocardial interstitium. Transthyretin amyloid cardiomyopathy,which is no typical clinical symptoms and signs,is mainly divided into mutant type and wild type. In order to improve the diagnosis and treatment practice and clinical research of transthyretin amyloid cardiomyopathy in China,this paper briefly introduces the latest diagnostic criteria and treatment methods of transthyretin amyloid cardiomyopathy around the world.更多还原