【摘要】 进行性家族性肝内胆汁淤积症是一组罕见的常染色体隐性遗传病,起病早,进展快,死亡率高,治疗较为困难。本文报道进行性家族性肝内胆汁淤积症3型2例,并附文献复习。更多还原

【Abstract】 Progressive familial intrahepatic cholestasis is a group of rare autosomal recessive genetic disease with early onset,rapid progression,high mortality and difficult treatment. This paper reported 2 cases of type 3 progressive familial intrahepatic cholestasis and literature review.更多还原