【摘要】 目的 :探讨肝脏遗传性出血性出血性毛细血管扩张症(HHHT)行肝动脉双重结扎缩扎术治疗方法及疗效。方法:2005年7月—2011年2月对6例HHHT患者行肝动脉双重结/缩扎术,并长期随访。结果:随访5～14年后,患者临床症状、实验室指标及影像学表现均得到不同程度的改善。结论:肝动脉起始和入肝处的双重结扎缩扎术能够有效地降低肺动脉压,减轻肝脏的损伤,是治疗HHHT的有效方法。更多还原

【Abstract】 Objective: To investigate the treatment and curative effect of double ligation/constriction of hepatic artery in hereditary hepatic telangiectasia. Methods: The clinical data of 6 patients with hereditary hemorrhagic telangiectasia who underwent double ligation/constriction of hepatic artery from July 2005 to February 2011 were analyzed retrospectively, and the prognosis of the patients who underwent surgical treatment was evaluated. Results: After 5-14 years of follow-up,the clinical symptoms, laboratory indicators and imaging manifestations of patients with double ligation/constriction of hepatic artery were all improved. Conclusion: The double ligation/constriction at the origin and entrance of hepatic artery in patients with hepatic HHT can effectively reduce pulmonary artery pressure and reduce liver injury. Double ligation/constriction of hepatic artery is an effective method to treat hereditary hemorrhagic telangiectasia of the liver.更多还原