【摘要】 目的探讨产前超声与解剖铸型在胎儿肺动脉发育异常诊断中的应用价值。方法回顾性分析35例胎儿肺动脉发育异常的产前超声图像,与解剖铸型标本对照,分析其特征及鉴别要点。结果胎儿肺动脉发育异常中,肺动脉及其分支大小异常30例(肺动脉狭窄18例,肺动脉闭锁9例,肺动脉瓣缺如综合征3例),肺动脉起源异常5例(一侧肺动脉缺如2例,肺动脉起自升主动脉2例,肺动脉吊带1例)。引产后病理解剖25例,血管铸型10例。超声误诊3例:肺动脉闭锁误诊为共同动脉干1例,肺动脉闭锁误诊为肺动脉狭窄1例,室间隔缺损型肺动脉闭锁肺血来源误诊1例。结论胎儿肺动脉发育异常中肺动脉闭锁和狭窄较为常见,产前超声对胎儿肺动脉发育异常具有重要诊断价值,解剖及铸型的反馈有助于进一步认识胎儿肺动脉发育异常。更多还原

【Abstract】 Objective To investigate the value of antenatal ultrasound and vascular cast,autopsy in diagnosis of pulmonary artery dysplasia(hereinafter referred to as PAD).Methods Thirty-five fetuses with prenatal-ultrasound-diagnosed PAD were enrolled in this study.Ultrasound images were retrospectively processed for analysis,comparing with autopsy and vascular cast.Results Among the 35 fetuses with PAD,30 of them were found dysplasia of pulmonary artery and its branches in pipe diameter(18 in stenosis,9 in atresia,3 in dilation),anomalous origin of pulmonary artery in 5 cases(absence of unilateral pulmonary artery in 2 cases,origin of pulmonary artery from ascending aorta in 2 cases,pulmonary artery sling in 1 case).Twenty-five cases underwent autopsy and 10 cases for vascular cast after termination.Three anomalies were misdiagnosed or missed diagnosed by ultrasound,one pulmonary atresia misdiagnosed as common arterial trunk,another one pulmonary atresia misdiagnosed as pulmonary stenosis,one blood supply of lung of pulmonary atresia with ventricular septal defect misdiagnosed.Conclusion Among the cases of PAD,pulmonary stenosis and atresia are most common.Antenatal ultrasound has significant diagnostic value in these cases.Feedback from autopsy and vascular cast is helpful for further understanding of PAD.更多还原