【摘要】 目的 :探讨颈椎MRI对Klippel-Feil综合征并发畸形和继发退变的诊断价值。方法 :采用1.5 T超导MRI仪对21例Klippel-Feil综合征行颈椎MRI,观察MRI各序列对Klippel-Feil综合征阻滞椎的显示情况,并分析是否合并附件、脊髓或椎管等其他发育畸形,以及有无椎间盘、黄韧带、椎管及脊髓等的继发退变。结果:Klippel-Feil综合征阻滞椎MRI典型征象呈"蜂腰状",21例阻滞椎以累及C3椎体为主,占47.62%(10/21),均合并附件分割不全,脊髓空洞症、颅底凹陷、先天性椎管狭窄及椎管内肠源性囊肿等其他发育异常或畸形各1例。21例中,继发椎间盘突出16例(76.19%),其中突出间盘位于阻滞椎以上5例(31.25%),位于阻滞椎以下11例(68.75%)。颈椎曲度变直14例(66.67%);黄韧带肥厚3例(14.29%)。结论:颈椎MRI不但可清晰显示Klippel-Feil综合征的先天阻滞椎及其并发畸形,还有助于准确评价继发的颈椎退行性改变,从而更好地指导临床治疗。更多还原

【Abstract】 Objective:To explore the diagnosis value of cervical MRI in Klippel-Feil syndrome complicated with malformation and secondary degeneration. Methods:The MRI manifestations of 21 cases Klippel-Feil syndrome were retrospectively analyzed.The MRI manifestations of block vertebrae were observed. The malformations of appendix,spinal cord or spinal canal and the secondary degenerations of intervertebral disc,ligamentum flavum,spinal canal or spinal cord were analyzed. Results:The MRI characteristic features of block vertebrae of Klippel-Feil syndrome mainly performed for "wasp waist shape",21 patients of block vertebrae mainly involving the C3 vertebral(47.62%,10/21). The block appendix occurred in all the 21 cases,and syringomyelia,basilar invagination,congenital spinal stenosis and intraspinal enterogenous cysts occurred once. In all 21 cases,16 cases had secondary intervertebral disc herniation(76.19%),of them,5 cases of disc herniation were above the block vertebral(31.25%),11 below(68.75%);cervical curvature straighten occurred in 14 cases(66.67%),ligamentum flavum hypertrophy in 3 patients(14.29%). Conclusion:MRI can clearly display the deformities and degeneration of spine of Klippel-Feil syndrome,and is helpful to guide clinical treatment.更多还原