【摘要】 目的分析多脾综合征(PS)的体部CT表现,提高对PS的认识和诊断水平,并结合影像表现,加深对其发病机制的理解。方法回顾性分析12例具有完整CT资料PS的病例。CT检查包括胸部和腹部平扫及增强扫描。重点观察胸腹部脏器和心血管异常及两者的关联性。结果 11例PS中4例心脏无异常,胸腹腔脏器异常表现包括:2例中位水平肝、中位胆囊,3例短胰,2例中肠旋转不良,1例对称性左肺。另外7例心脏存在异常,其中3例为单一性心脏异常,4例为复杂型心脏病;胸腹腔脏器异常表现包括:4例中位水平肝,2例左位肝,3例中位胆囊,1例胆囊缺如,2例左位胆囊,6例短胰,2例中肠旋转不良,4例对称性左肺。11例均见多脾、肝段下腔静脉缺如伴奇静脉/半奇静脉异常连接,其中脾脏5例位于左上腹,6例位于右上腹,胃与脾脏的位置一致。结论 PS是一组多系统畸形,胸腹部CT增强扫描有助于全面的诊断;存在心脏异常者,应行单独的心脏扫描。更多还原

【Abstract】 Objective To analyze the imaging findings of polysplenia syndrome on thoracic and abdominal CT. Methods CT of 11 patients with polysplenia syndrome was reviewed to correlate the visceral and cardiac anomalies. Results In 4 patients without cardiac abnormality, the liver was symmetrically positioned in the midline with midline gallbladder(2), short pancreas(3), midgut malrotation(2) and symmetrical left lung(1) on CT. Ofthe remaining 7 patients with simple(3) and complex(4) cardiac anomaly,CT showed abdominal visceral anomaly in 6 including symmetrical midline liver(4) or left upper abdominal liver(2), gallbladder aplasia(1), midline(3) or left-sided(2) gallbladder, short pancreas(6), midgut malrotation(2), and symmetrical left lung(4).Multiple spleens and absent hepatic inferior vena cava with azygos or hemiazygos continuation were found in all 11 patients..The spleens were located in the left(5) or right(6)upper abdomen with the stomachs on the same sides as the spleens in all 11 cases.Conclusion Contrast enhanced thoraco-abdominal CT is useful for evaluating cardiac and abdominal visceral anomalies in polysplenia syndrome.更多还原