Purpose To investigate the clinicopathological features,treatment and prognosis of perivascular epithelioid cell tumor( PEComa) of the head and neck. Methods Two cases of PEComa were analyzed by studying clinical data,histopathologic and immunohistochemical( En Vision) changes and the related literatures were reviewed. Results Case 1 was a 26-year-old woman with a recurrent larynx tumor,and case 2 was diagnosed in a 56-year-old man with a left nasal cavity mass. Their tumors were well-demarcated,and ranged ...