【摘要】 目的探讨Hallervorden-Spatz综合征的颅脑MRI诊断价值,提高对该病的认识。方法回顾性分析2007年2月~2012年4月经临床证实为Hallervorden-Spatz综合征的4例患者颅脑MRI资料。结果 Hallervorden-Spatz综合征颅脑MRI表现为:双侧苍白球、黑质T2WI像对称性低信号,苍白球低信号的前内侧出现斑点状高信号,即典型的"虎眼征"。SWI像上病灶呈低信号,MRS检查可见NAA、NAA/Cr及Cho/Cr下降。结论 Hallervorden-Spatz综合征具有典型的MRI表现,MRI检查在Hallervorden-Spatz综合征中有重要的诊断价值。更多还原

【Abstract】 Objective To investigate the diagnostic value of MRI in Hallervorden-Spatz syndrome.Methods MRI data of Hallervorden-Spatz syndrome in 4patients in our hospital from February 2007to April 2012were retrospectively analyzed.Results The brain MRI of Hallervorden-Spatz syndrome was demonstrated abnormalities confined to the pallidum,which presented diffuse low signal intensity in SWI,and eye-of-the-tiger sign in T2WI.Compared with the normal brain tissue,the NAA,NAA/Cr,Cho/Cr were decreased.Conclusion Hallervorden-Spatz syndrome has definite MR imaging findings,and MRI is of important value in diagnosis of Hallervorden-Spatz syndrome.更多还原