【摘要】 目的探讨罕见病骨斑点症的X线表现特点。方法回顾性分析经证实的4例骨斑点症患者临床及影像学资料,并结合文献复习。结果病变常对称性分布于肢体的两侧。其典型影像特征为X线表现为数毫米至1 cm大小不一的圆形和卵圆形致密影,常见于长骨骨骺、干骺端、骨盆、腕骨、跗骨及手足小管状骨骨松质内,骨干少见,按应力线分布且呈对称性,不累及皮质。CT能清楚显示骨松质中的斑点样硬化灶,较X线能更准确反映病灶在骨内的分布,有无累及骨皮质,骨膜及周围软组织情况。结论该病多具有典型的影像表现,常规X线检查可以提供满意的诊断信息。更多还原

【Abstract】 【Objective】To investigate the X-ray features of osteopoikilosis(rare disease).【Methods】Retrospective analysis confirmed four cases of Osteopoikilosis clinical and imaging data,combined with literature review.【Results】The lesions usually symmetry distributed in the both sides of the limbs.Typical imaging features of X-ray show number of millimeters to 1cm sizes of round,oval dense shadow distributed in long bone epiphysis,metaphysic,pelvis,wrist,tarsal bones,small tubular bone spongy bone in hand and foot,but the backbone is rare.The distribution is according to the stress distribution and the symmetric line,not involving the cortical bone.CT can clearly showed the spongy bone lesion as sclerosis spots.Compared with X ray,CT was more accurately reflecting the distribution of lesions in bone,whether involving the cortical bone,periosteum,and soft tissue conditions.【Conclusions】 There are typical imaging findings in osteopoikilosis,routine X-ray examination can provide satisfactory diagnostic information.更多还原