【摘要】 目的 探讨淋巴管肌瘤病的临床特点及螺旋CT表现,提高对本病的认识和诊断水平。方法 回顾性分析16例经手术、病理或临床诊断的淋巴管肌瘤病患者的多脏器的CT表现。结果 16例均见双肺多发圆形、类圆形低密度含气囊腔影,4例气胸,4例肺野呈磨玻璃影,8例胸腔积液,2例出现肺结节;11例合并肾血管平滑肌脂肪瘤,其中2例合并肝血管平滑肌脂肪瘤;2例合并结节性硬化;3例腹腔见多发淋巴结影;3例囊状淋巴管瘤。结论 淋巴管肌瘤病的胸腹部MSCT表现具有一定的特征,MSCT检查对该病的诊断及鉴别诊断具有重要的价值。更多还原

【Abstract】 Objective To investigate the clinic and MSCT characteristics of lymphangioleiomyomatosis,and to improve the knowledge and diagnostic awareness.Methods The CT findings of 16 cases with lymphangioleiomyomatosis who were pathologically proved and clinically diagnosed,were analyzed retrospectively.Results There were different typical CT findings in 16 patients,including multiple thin-walled lung cysts(n=16),4 cases with pneumothorax,4 cases with lung ground-glass opacity,8 cases with pleural effusion,2 cases with pulmonary nodules;11 cases with renal angiomyolipoma,including 2 cases with liver angiomyolipoma,2 cases associated with brain tuberous sclerosis,3 cases of abdominal multiple lymph node,3 cases of cystic lymphangioma.Conclusion Pulmonary and abdominal MSCT characteristics provided important information in the diagnosis of lymphangioleiomyomatosis.MSCT examination plays an important value in diagnosis and differential diagnosis of this disease.更多还原