【摘要】 目的探讨烟雾病伴发动脉瘤的诊断和治疗。方法回顾性分析6例烟雾病合并颅内动脉瘤患者的临床表现、影像学特点及治疗方法。结果6例中5例表现为颅内出血,1例表现为缺血症状;其中外周动脉型2例,大动脉型4例。3例行显微外科手术治疗,1例行血管内栓塞治疗,均获良好效果。结论DSA是确诊烟雾病伴发动脉瘤的金标准。3D-DSA可提高伴发动脉瘤的检出率,清晰显示动脉瘤的立体形态、瘤颈和与载瘤动脉的关系。大动脉型者可用显微外科手术治疗或血管内栓塞治疗,外周动脉型者的治疗,有待进一步探讨。更多还原

【Abstract】 【Objective】To discuss the diagnosis and treatment of moyamoya disease accompanied with intracranial aneurysm. 【Method】Retrospectively analysed the clinical manifestation,imaging characteristic and therapeutic method of 6 cases. 【Reseults】5 cases presented with intracranial hemorrhage,1 case presented with ischemic symptoms. Aneurysm located on peripheral artery in 2 cases and on main artery in 4 cases. 3 cases underwent microsurgical treatment,1 case underwent endovascular therapy,all cases achieved good outcome.【Conclusions】DSA is the golden standard to diagnose moyamoya disease accompanied with aneurysm. 3D-DSA can improve the finding of aneurysm and show its stereo configuration and the relationship between aneurysm nech and the artery. Aneurysms on main artery can be treated by microsurgical operation or endovascular embolization; but the therapy of aneurysm on peripheral artery need further study.更多还原