【摘要】 目的提高对肺泡蛋白沉积症(pulmonary alveolar proteinosis,PAP)的认识。方法通过1例患者的诊治,结合文献复习就本病的临床特点、影像学特征、诊断方法以及治疗和预后进行分析。结果PAP是一种病因及发病机制未明,临床表现无特征性表现,以咳嗽、咳痰、气促为多见,影像学不易鉴别的罕见疾病。结论PAP发病率较低,起病隐匿,临床症状和实验室检查及影像学缺乏特征性,确诊困难,临床容易误诊或漏诊。更多还原

【Abstract】 Objective To improve the understangding of pulmonary alveolar proteinosis,(PAP).Methods By case-study method and literature review and clinical analysis of 1 patients with PAP,to investigate clinical manifeststions,image feature,method of diagnosis,treatment and prognosis of PAP.Results PAP is rare disease and its pathogensis remained unknown.Conclusion PAP is easy to be misdiagnosed in pulmonary disease because of no specific clinical manifestations and image feature.We should improve the knowledge about the PAP.更多还原