【摘要】 目的:探讨耳蜗性耳硬化症的临床特点。方法:结合文献复习,报告3例2007年3月-2008年10月诊治的经高分辨颞骨CT确认的耳蜗性耳硬化症患者。结果:3例以反复发作性眩晕或(和)平衡障碍为首要主诉,同时有进行性听力下降病史。2例(各1耳)为单纯感音神经性聋,考虑为"纯"耳蜗性耳硬化症,其余为伴不同程度骨导下降的混合性聋。高分辨颞骨CT的特点:耳蜗、前庭、半规管及内耳道等部位可见低密度区,耳蜗区呈现"晕影"征或"双环"征,密度有不均。结论:对不能解释原因的感音神经性聋、存在前庭症状的混合性聋并呈进行性听力下降的慢性病史者应考虑耳蜗性耳硬化症的可能,CT对耳蜗性耳硬化症的临床诊断有重要价值。更多还原

【Abstract】 Objective:To investigate the clinical features in cochlear otosclerosis.Method:Three cases with cochlear otosclerosis in our hospital from March 2007 to October 2008 were reported and the relevant literatures were reviewed. All the cases were confirmed the diagnose by temporal bone high-resolution CT scan(HRCT).Result:The chief complaint when visited was recurrent episodic vertigo or equilibrium disturbance with progressing hearing loss in all cases. Two ears in 2 cases were simple sensorineural deafness and considered the pure cochlear otosclerosis.Others were mixed deafness with the descent of bone conduction in different extent. The characters in HRCT :the low density area could be seen in different areas of the otic capsule ,the pericochlear lucency or double-ring effect were the typical signe.Conclusion:The diagnosis of cochlear otosclerosis is considered in the insoluble sensorineural deafness and the mixed deafness with vestibular symptoms and chronic hearing loss history. Temporal bone HRCT plays an important role in the clinical diagnosis of cochlear otosclerosis.更多还原