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心脏淀粉样变性的超声表现与临床特点

Ultrasonic appearance and clinical characteristics of cardiac amyloidosis

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【作者】 陈雪梅白旭东赵丽荣

【Author】 CHEN Xue-mei,BAI Xu-dong,ZHAO Li-rong(Department of Ultrasound,the First Hospital of Jilin University,Changchun 130021,China)

【机构】 吉林大学第一医院

【摘要】 目的:探讨心脏淀粉样病的声像图特征及临床观察结果,进一步提高疾病诊断的准确率。方法:应用彩色多普勒超声心动图,观察5例心脏淀粉样变性(CA)患者的超声表现,并观察生化指标及临床表现,同时进行病理活检。结果:本文5例患者均左房增大,心室肥厚,左室收缩功能降低,小到中等量的心包积液;心肌超声组织特征为小斑点或颗粒状星点样,心外活检表现为刚果红染色阳性。结论:中老年患者出现不明原因的充血性心力衰竭,应进行彩色多普勒超声心动图观察,以免遗漏心脏淀粉样变的诊断,有助于临床确诊治疗。

【Abstract】 Objective To analyze the clinical characteristics and ultrasonic appearance of patients with cardiac amyloidosis,and raise accurate rate of disease diagnosis gradually.Method The ultrasonic appearance and the clinical data of 5 patients with cardiac amyloidosis,also the biochemical indicators and pathology were overviewed.Results The patients with cardiac amyloidosis had changes including characteristics of large left atriums,hypertrophic ventricular walls,lower systolic function of left ventricle in echocardiography,pericardial effusion(little to medium dose),and cardiac muscle had speckle or granulation in ultrasonic characteristics.Biopsy was developed staining of Congo Red.Conclusion The old patients of backward failure with the characteristics in echocardiogram,carry out Doppler echocardiography observation,in order to avoid missing cardiac amyloidosis to diagnose,conduce to clinical diagnose and treatment.

【关键词】 心脏淀粉样变性超声心动图
【Key words】 HeartAmyloidal degenerationEchocardiogram
  • 【文献出处】 吉林医学 ,Jilin Medical Journal , 编辑部邮箱 ,2009年03期
  • 【分类号】R541;R445.1
  • 【被引频次】1
  • 【下载频次】131
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