【摘要】 目的了解国内副肿瘤性天疱疮的临床特点。方法通过计算机检索,总结国内24例副肿瘤性天疱疮患者的临床表现、辅助检查及治疗。结果Castleman瘤是我国副肿瘤性天疱疮患者最常伴发的肿瘤,其次是淋巴瘤、慢性淋巴细胞白血病;临床上副肿瘤性天疱疮常误诊的疾病依次是扁平苔藓、多形红斑和大疱性皮肤病;闭塞性细支气管炎是副肿瘤性天疱疮患者的主要死亡原因。结论早期诊断、治疗肿瘤和预防闭塞性细支气管炎是治疗副肿瘤性天疱疮的关键。更多还原

【Abstract】 Objective To obtain a better understanding the features of paraneoplastic pemphigus in China.Methods The clinical manifestation,auxiliary examination and treatment of 48 cases with paraneoplastic pemphigus were analyzed by computer index.Results It was shown astleman tumor of the most common concomitant neoplasm in China,then lymphoma and chronic lymphocytic leukaemia.Paraneoplastic pemphigus was frequently misdiagnosed as lichen planus,erythema polymorphe and bullous dermatosis in order.Obliterative bronchiolitis was the major death factor of paraneoplastic pemphigus.Conclusions The early diagnosis,treating tumor and preventing obliterative bronchiolitis are essential for management of paraneoplastic pemphigus.更多还原