【摘要】 目的探讨肺淋巴管肌瘤病的影像学特征,提高对该病的诊断水平。方法回顾性分析我院确诊的肺淋巴管肌瘤病11例,全部病例均行胸部X线检查及胸部HRCT检查。结果胸部X线表现无明显特异性。HRCT的特征性表现为双肺弥漫分布的圆形或多边形囊腔,囊腔直径2-4 0mm左右,大多数小于1 0mm,囊壁厚度小于1mm。结论肺淋巴管肌瘤病是一种罕见病,其影像学表现具有特征性,影像学检查尤以HRCT检查对该病的诊断具有重要的意义。更多还原

【Abstract】 Objective to investigate image features of pulmonary lymphangioleiomyomatosis(PLAM) and to improve its diagnosis.Methods eleven patients with pathologically proved PLAM underwent chest X-ray and high resolution thoracic CT scanning,The clinical data and image features were retrospectively analyzed. Results The chest X-ray shows no characteristic manifestation,the characteristic HRCT manifestation was multiple,different sized cystoid transparent areas,which were diffusely distributed throughout both lungs.Most cysts were less than 10mm in diameter (2-40mm),the cysts cliff were less then 1mm.Conclusion PLAM is a rare disease, image examinations have characteristic signs especially HRCT更多还原