【摘要】 目的:探讨血管外皮细胞瘤(HPC)的临床、病理、影像学特征及治疗方法。方法:分析1例颅内HPC复发合并肺多发转移病例并结合文献复习予以探讨。结果:颅内HPC复发合并肺多发转移病例临床罕见。影像学表现与脑膜瘤易混淆,MRI表现为T1WI等低信号,T2WI不均匀等高信号,多可见"硬膜尾征"和血管流空信号。病理学特点为梭形细胞,小血管鹿角样分支。本病是少数可转移至中枢神经系统以外的颅内原发肿瘤,有复发和转移倾向。病灶切除应彻底,并辅以放疗。结论:颅内HPC是一种具有高复发率和易发生颅外转移的肿瘤,包括颅脑和肺、骨、肝等是易转移靶器官。更多还原

【Abstract】 Aim:To study on clinical,pathological,radiological feature and trearnent of the hemangiopericytoma (HPC).Methods:A case of intracranial hemangiopericytoma recurrence with pulmonary metastasis was reported,and literatures were reviewed.Results:Intracranial hemangiopericytoma recurrence with pulmonary multiple metastasis is rare.HPCs are usually misdiagnosed as meningiomas in radiological findings.MRI: Hypo-isointensity on T1WI,heterogeneous iso-hyperintensity on T2WI,a"dural tail"sign and vascular void flow can be found in MR images.The spindle tumor cells and antler-Eke ramification can be found in pathology. Intracranial HPC is one of the rare primary intracranial tumors which can metastasize outside of the central nervous system.The character of recurrence and metastasis of the disease requires enbloc resection and adjuctive radiotherapy.Conclusion:Intracranial hemangiopericytoma is a tumor with highly recurrence and metastasis.The recurrence and metastasis of HPC often occur in sites such as lung,bones and liver.更多还原