【摘要】 目的探讨腹膜后囊性淋巴管瘤的诊断与治疗。方法收集经病理证实的成人腹膜后囊性淋巴管瘤7例,回顾性分析其临床特征及影像学表现,并与手术、病理结果对照。其中男2例,女5例,平均年龄51岁。患者均无特征性临床表现。超声及CT均表现为边缘光整的囊性肿块,病变大小约6cm×7cm～20cm×21cm,部分囊内有分隔,且壁与分隔可部分强化。术前诊断腹膜后囊性占位病变4例,腹腔囊肿2例,仅1例患者经CT引导下穿刺抽液确诊。结果7例均行手术治疗,完整切除肿瘤者6例,1例因肿瘤浸润肝脏及胰腺仅行大部切除。术后病理报告证实为:(腹膜后)囊性淋巴管瘤。7例随访9个月～10年,完整切除者均未见复发,大部切除者于术后5个月出现局部复发。结论超声及CT对腹膜后囊性淋巴管瘤定位、定性诊断具有重要价值,手术切除是治疗首选。更多还原

【Abstract】 Objective To evaluate the diagnosis and treatment of retroperitoneal cystic lymphangioma. Methods A retrospective study of clinical characteristics and imaging findings of pathologically proved cystic lymphangiomas in 7 adults (2 males and 5 females;mean age,51 years) was conducted,and comparisons were made between these findings and operative and pathological results.All the patients presented no special clinical manifestation.Ultrasonography and CT scan showed smoothly margined cystic masses ranging from 6 cm×7 cm to 20 cm×21 cm;some of them had septums, and the walls and septums could be partially enhanced. Preoperative definite diagnosis was made in only 1 case by CT-guided percutaneous catheter drainage of the lymphangioma; while the others were misdiagnosed as abdominal cavity cysts(2 cases)and retroperitoneal space-occupying cystic lesions(4 cases). Results Complete extirpation was performed in 6 cases,and subtotal cystectomy,in 1 case because of the liver and pancreas involvement by the tumor.Postoperatively,all the lesions were pathologically proved to be retroperitoneal cystic lymphangioma.There was no recurrence during the follow-up of 9 months to 10 years,except for 1 case undergoing subtotal cystectomy who had local recurrence 5 months after operation. Conclusions Ultrasonography and CT are the most useful imaging modality for locating the site and determining the nature of lymphangioma . Surgical excision is the first choice for the treatment.更多还原