【摘要】 目的　研究出血性烟雾病的出血机制及检查诊断方法。方法　对 6 7例颅内出血患者经头部CT和脑动脉血管造影检查 ,部分病例经腰穿检查。结果　 6 7例患者诊断为烟雾病 ,其累及血管为单侧、双侧颈内动脉分支和 (或 )椎动脉分支 ,其病变区出现异常增生的小血管 ,CT检查患者颅内有不同部位出血灶。结论　烟雾病的诊断方法主要为全脑动脉血管造影。更多还原

【Abstract】 Objective To study the diagnostic method and bleeding mechannism of the hemorhagic moyamoya disease.Methods Head CT, cerebral arteriography for all and partial lumbar CSF (cerebral spinal fluid) centesis was undertaken in 67 cases of intracranial hemarhage. Results 67 cases of hemorrhagic moyamoya disease always involved unilateral or bilateral internal caroltid and/or vertebral arterial branches with abnormal hyperplasia of small vessels at the same area. CT scane showed intracranial hemorrhagic foci in different parts clearly. Vasculitis caused by immunologic effect led to cerebral arterial stenosis or occlusion with compensatory small vascular hyperpulasia. The mechanism of thinning of these vascular walls enlargement of vascular lumen, rupture of miliary or cystic anourysms and infraependymal infarctions were due to bleeding and rebleeding.Conclusion Percuteneous pancerebral arteriography is the main diagnostic method for Moyanoyas disease.更多还原