【摘要】 目的　总结胸腺类癌引起的异位ACTH综合征临床表现 ,提高对此综合征的诊断率。方法分析 6例患者的临床表现 ,尤其是非典型胸腺类癌所致异位ACTH综合征的症状和体征、实验室相关测定值以及影像学表现。结果　 6例患者均行胸腺肿瘤切除术并经病理证实为胸腺类癌导致异位ACTH综合征。结论　有明确库欣综合征临床表现 ,且伴有低血钾 ,浮肿 ,蛋白尿且出现不能解释的 8mg地塞米松抑制试验不被抑制 ,均应考虑异位ACTH综合征 ,胸腺类癌是异位ACTH综合征的可能病因。更多还原

【Abstract】 Objective To increase the awareness of ectopic ACTH syndrome in patients with thymus carcinoid. Methods Clinical manifestations, especially atypical presentation of ectopic ACTH syndrome, laboratory findings and imaging data (chest X-ray and CT, etc.) in 6 patients were analysed. Results In all 6 patients, the thymus tumors removed were pathologically proved to be thymus carcinoid. Conclusion Patients having typical manifestations of Cushing′s syndrome with hypokalemia, edema, proteinuria and equivocal result of dexamethasone inhibition test, should be considered as ACTH syndrome. And thymus carcinoid seems to be the cause of the disease.更多还原