【摘要】 目的　探讨 Caroli病的临床特点和诊治方法。方法　 1 1例 Caroli病人 ,对其临床资料进行回顾性总结。结果　曾有胆道手术史 3例 ,合并胆道结石 6例 ,癌变 4例 ,合并肝外胆管囊肿 5例 ,左肝局限囊状扩张 5例 ,中肝 5例 ,弥漫性胆管囊状扩张 1例。手术治疗 9例 ,采用胆总管囊肿切除 +中肝部分切除或左肝外侧叶切除 +胆肠内引流 4例 ,单纯肝外囊肿切除+内引流 1例 ,另 4例合并癌变病人 ,胆总管切开清除癌组织 +T管引流 2例 ,探查活检 2例。结论　提高对 Caroli病的认识 ,减少误诊误治 ,降低癌变率 ,手术切除囊状扩张病灶 ,重建胆肠通道是有效治疗手段更多还原

【Abstract】 Objective To study clinical features and therapeutic methods of Caroli Disease.Methods Clinical data of 11 patients were summarized retrospectively.Result 3 cases had the history of bile tracts operation,6 cases were associated with bile duct stones, 4 cases with oncogenesis,5 cases with extraheptic bile duct cyst.5 cases had confined segmental cystic dilatation of intrahepatic bile duct in the left lobe,5 in the middle lobe.1 case had diffused multifocal dilatation in the whole liver. 9 patients underwent operation that included the resection of common bile duct,partial hepatectomy in the middle lobe or in the left lateral lobe and bile enteric drainage in 4 cases.1 patient underwent resection of extraheptic bile duct cyst and bile enteric drainage.4 patients associated with chologiocarcinoma,2 cases underwent choledochotomy to remove the tumor and T tube drainage.2 cases underwent exploration and biopsy.Conclusions Improvement on recognition of Caroli Disease can decrease the rate of false diagnosis,false therapy and oncogenesis.Resection of cystic dilatation and reconstruction of bile enteric drainage are efficacious ways to treat the disease.更多还原