【摘要】 先天性主动脉褶叠临床少见，作者收治５例。此病患者胸骨左缘和肩胛间区可闻及收缩期杂音，均有不同程度的右上肢高血压。胸部Ｘ线片示左上纵隔影增宽。主动脉造影可见弓降部主动脉过长、槽叠和不同程度的瘤样扩张，其中１例瘤体破裂形成假性动脉瘤。３例合并弓部缩窄。１例合并降主动脉始部缩窄，１例合并主动脉弓中断。４例在左心转流下置入人工血管，１例在深低温停循环下完成手术。术后均恢复良好。作者就该病的临床特点、解剖特征、手术方法和术后处理等进行了扼要讨论。更多还原

【Abstract】 Abstract5 patients with congenital kinking of the aorta,one male and 4 females with a mean age of 29 years(age range , 10～37 years),underwent surgical-treatment.There was a svstolic murmur at the leftsternal border and the interscapular area and hyperten-sion only in the right arm.A chest rentgenogramshowed a widened left superior mediastinum.Angiograms showed eIongation,kinking and aneurysmformation of the aortic arch and descending aorta andthe aneurysm ruptured in one. Three patients were as-sociated with coarctation of the aortic arch,one withcoarctation of the upper descending aorta and anotherwith interruption of the aortic arch. All the patientsh6an excellent results.The clinical features,mor-phology,surgical techniques and postoperative carewere discussed.更多还原