【摘要】 本文对25例先天性双腔右心室(DCRV)的彩色血流多普勒超声心动图的表现进行分析。7例胸骨旁主动脉根短轴面观显示主动脉侧的右室心肌呈舌状增厚突向心室腔,与其对应的右室前壁心肌呈楔形肥厚,二者之间形成狭窄孔。6例心尖四腔观,右室游离壁和室间隔中部均呈局限性舌状增厚,突向右室腔,这突出的肌块将右室腔分成两部分,即三尖瓣下的近侧腔和肌块远端的远侧腔,其间形成狭窄孔,突出肌块近侧的室间隔于收缩期向左侧弯突,于舒张期呈扁平状,12例有以上两个切面中的异常肥厚心肌的表现,本病合并室间隔缺损20例、肺动脉瓣狭窄4例、房间隔缺损和三尖瓣狭窄1例。彩色血流多普勒影象对本病诊断很有助益,20例的心尖四腔观发现二股相互靠近但方向相反的血流,即一股穿越异常肌束狭窄孔的喷泉状花色射流和一股经三尖瓣口的蓝花色返流。更多还原

【Abstract】 The analysis were performed on the colour flow Doppler echocardiographic features of congenital double chambered right ventricle (DCRV). In 7 cases, the parasternal short axis view at the level of aortic root revealed the anomalous tongue-shaped right ventricular muscle mass proturding from the aortic side into the cavity of right ventricle (RV) which was over against the wedge-shaped muscle mass protruding from the anterior wall of the RV. In 6 cases, the apical four chamber view revealed two local tongue-shaped muscle masses protruding from the free wall of the RV and the middle portion of IVS respectively. The protruding muscle masses of the RV and the IVS divided the cavity of the RV into two chambers, a proximal chamber just below the tricuspid valve and a chamber distal to the anomalous muscle. A stenosed orifice was formed between the proximal chamber and the distal chamber. The IVS proximal to the protruding muscle masses curved convex toward the LV at the end-systole and become flat at diastole. In 12 cases, there are above-mentioned echocardiographic features of anomalous hypertrophic muscles. DCRV may coexist with a VSD in 20 cases, PS in 4, ASD and tricuspid stenosis in 1. Colour flow Doppler imaging is very useful for diagnosing DCRV. In 20 cases, the apical four chamber view revealed that two steams of flow are close but in the reverse direction in systole. A mosaic fountain-shaped flow jet passed through the stenosed orifice of the anomalous muscles and a bluish mosaic regurgitation passed through the tricuspid orifice. In the article, we disucssed the pathoana-tomy, echocardiographic features, type and the differential diagnosis of DCRV.更多还原