【摘要】 结合6例Shy—Drager 综合征,提出了诊断本病的6个要点。在6例中,最年青者起病年龄为 11岁,该例表现明显的植物神经症状及特殊分布的肌萎缩。3例电子计算机X线断层脑扫描检查发现有广泛性脑萎缩。认为本病发病机理为原发性神经系统病变而非继发于缺氧所致;本病为一独立疾病,应与原发性直立性低血压加以区别。更多还原

【Abstract】 According to the clinical features of six cases of Shy-Drager syndrome, six main points may be summed up in this disease. Among the six patients,the youngest female patient who had the symptoms at the age of 11 showed prominent autonomic nervous symptoms and peculiar distribution of muscle atrophy. CT scanning of 3 cases showed diffuse brain atrophy. It is thought that the pathogenesis of the disease was the primary degenerative process rather than secondary degeneration due to anorexia; the disease was an independent clinical entity,and should be separated from idiopathic orthostatic hypotension.更多还原