【摘要】 <正> 急性分化性组织细胞增生症,是一种急性进行性、系统性、分化性组织细胞增生性疾病。常见于3岁以内婴幼儿,少数为新生儿。本病的基本病理特点为单核巨噬细胞增生和浸润,累及多个器官和组织,亦可仅侵犯某一器官,预后很差,病儿常在短期死亡。我教研室1964～1980年来共尸检11例,均经病理组织学确诊为网状细胞增生症及更多还原

【Abstract】 Eleven cases(8 males and 3 femals)of acute differentiated histiocytosis were aut-opsied and studied.Nine out of 11 cases examined were under 2 years of age.Fever,anemia,thrombocytopenia and eruptions were the usual clinical features.Cutaneousnodules appeared only in 1 case.Autopsy findings revealed that the lungs were most seriously affected,ten out of11 cases had pulmonary lesions,in which 2 had honey-comb lungs,The other usuallyaffected organs were liver(9 cases)spleen(10 cases),deep lymph nodes(11 cases)specially the mesentric lymph nodes,and(?) the thymus(9 cases:one of them showed“cvstic”change).The nomenclature and diagnosis of this disease were briefly discussed and factorsinfl(?)encing the prognosis were analysed更多还原